{"created":"2023-07-27T06:28:53.349374+00:00","id":13478,"links":{},"metadata":{"_buckets":{"deposit":"ada1aafa-e6b8-4042-8008-3fceb28147bb"},"_deposit":{"created_by":3,"id":"13478","owners":[3],"pid":{"revision_id":0,"type":"depid","value":"13478"},"status":"published"},"_oai":{"id":"oai:kanazawa-u.repo.nii.ac.jp:00013478","sets":["1132:1133:1134"]},"author_link":["20107","22206","22207","92"],"item_4_biblio_info_8":{"attribute_name":"書誌情報","attribute_value_mlt":[{"bibliographicIssueDates":{"bibliographicIssueDate":"1988-01-01","bibliographicIssueDateType":"Issued"},"bibliographicIssueNumber":"11","bibliographicPageEnd":"1725","bibliographicPageStart":"1721","bibliographicVolumeNumber":"77","bibliographic_titles":[{"bibliographic_title":"日本内科学会雑誌 = The Journal of the Japanese Society of Internal Medicine"}]}]},"item_4_description_21":{"attribute_name":"抄録","attribute_value_mlt":[{"subitem_description":"進行性全身性硬化症の経過中に原発性汁性胆肝硬変症を合併した1例を報告する.症例は42才,女性で, 25才頃より強指症が出現,その後全身の皮膚硬化,色素沈着およびレイノー現象が出現した.一方40才頃より健診で肝機能異常を指摘され,精査目的で入院,抗ミトコンドリア抗体陽性で,肝生検によりScheuer分類第2期の原発性胆汁性肝硬変症と診断された.また皮膚生検等によりBarnett II型の進行性全身性硬化症,いわゆるacrosclerosisと診断された.さらに家族検索において女性全員に免疫異常を認め,また同胞にシェーグレン症候群を認めた.これらの疾患の関連性および遺伝的背景について検討した.","subitem_description_type":"Abstract"}]},"item_4_publisher_17":{"attribute_name":"出版者","attribute_value_mlt":[{"subitem_publisher":"The Japanese Society of Internal Medicine = 日本内科学会"}]},"item_4_relation_12":{"attribute_name":"DOI","attribute_value_mlt":[{"subitem_relation_type":"isIdenticalTo","subitem_relation_type_id":{"subitem_relation_type_id_text":"10.2169/naika.77.1721","subitem_relation_type_select":"DOI"}}]},"item_4_relation_28":{"attribute_name":"関連URI","attribute_value_mlt":[{"subitem_relation_type_id":{"subitem_relation_type_id_text":"https://www.jstage.jst.go.jp/browse/naika/-char/ja/","subitem_relation_type_select":"URI"}},{"subitem_relation_type_id":{"subitem_relation_type_id_text":"http://www.naika.or.jp/","subitem_relation_type_select":"URI"}},{"subitem_relation_type_id":{"subitem_relation_type_id_text":"http://ci.nii.ac.jp/naid/130000901315/","subitem_relation_type_select":"URI"}}]},"item_4_rights_23":{"attribute_name":"権利","attribute_value_mlt":[{"subitem_rights":"Copyright © The Japanese Society of Internal Medicine 日本内科学会"}]},"item_4_source_id_11":{"attribute_name":"NCID","attribute_value_mlt":[{"subitem_source_identifier":"AN00195836","subitem_source_identifier_type":"NCID"}]},"item_4_source_id_9":{"attribute_name":"ISSN","attribute_value_mlt":[{"subitem_source_identifier":"0021-5384","subitem_source_identifier_type":"ISSN"}]},"item_4_version_type_25":{"attribute_name":"著者版フラグ","attribute_value_mlt":[{"subitem_version_resource":"http://purl.org/coar/version/c_970fb48d4fbd8a85","subitem_version_type":"VoR"}]},"item_creator":{"attribute_name":"著者","attribute_type":"creator","attribute_value_mlt":[{"creatorNames":[{"creatorName":"真田, 宏人"}],"nameIdentifiers":[{}]},{"creatorNames":[{"creatorName":"上野, 敏男"}],"nameIdentifiers":[{}]},{"creatorNames":[{"creatorName":"竹田, 亮祐"}],"nameIdentifiers":[{},{},{}]},{"creatorNames":[{"creatorName":"中沼, 安二"}],"nameIdentifiers":[{},{},{}]}]},"item_files":{"attribute_name":"ファイル情報","attribute_type":"file","attribute_value_mlt":[{"accessrole":"open_date","date":[{"dateType":"Available","dateValue":"2017-10-03"}],"displaytype":"detail","filename":"ME-PR-NAKANUMA-Y-1721.pdf","filesize":[{"value":"1.1 MB"}],"format":"application/pdf","licensetype":"license_note","mimetype":"application/pdf","url":{"label":"ME-PR-NAKANUMA-Y-1721.pdf","url":"https://kanazawa-u.repo.nii.ac.jp/record/13478/files/ME-PR-NAKANUMA-Y-1721.pdf"},"version_id":"d0f405f6-0fc9-4ef2-ab95-ddeba1a869af"}]},"item_language":{"attribute_name":"言語","attribute_value_mlt":[{"subitem_language":"jpn"}]},"item_resource_type":{"attribute_name":"資源タイプ","attribute_value_mlt":[{"resourcetype":"journal article","resourceuri":"http://purl.org/coar/resource_type/c_6501"}]},"item_title":"進行性全身性硬化症に合併した原発性胆汁性肝硬変症の1例","item_titles":{"attribute_name":"タイトル","attribute_value_mlt":[{"subitem_title":"進行性全身性硬化症に合併した原発性胆汁性肝硬変症の1例"},{"subitem_title":"A case of primary biliary cirrhosis associated with progressive systemic sclerosis","subitem_title_language":"en"}]},"item_type_id":"4","owner":"3","path":["1134"],"pubdate":{"attribute_name":"公開日","attribute_value":"2017-10-03"},"publish_date":"2017-10-03","publish_status":"0","recid":"13478","relation_version_is_last":true,"title":["進行性全身性硬化症に合併した原発性胆汁性肝硬変症の1例"],"weko_creator_id":"3","weko_shared_id":-1},"updated":"2023-07-28T01:04:17.475550+00:00"}