{"created":"2023-07-27T06:29:00.700389+00:00","id":13652,"links":{},"metadata":{"_buckets":{"deposit":"f42f2255-0903-42f2-ad02-efb04f99a99f"},"_deposit":{"created_by":3,"id":"13652","owners":[3],"pid":{"revision_id":0,"type":"depid","value":"13652"},"status":"published"},"_oai":{"id":"oai:kanazawa-u.repo.nii.ac.jp:00013652","sets":["1132:1133:1134"]},"author_link":["22793","468","22791","210","22792"],"item_4_biblio_info_8":{"attribute_name":"書誌情報","attribute_value_mlt":[{"bibliographicIssueDates":{"bibliographicIssueDate":"2012-04-01","bibliographicIssueDateType":"Issued"},"bibliographicIssueNumber":"7","bibliographicPageEnd":"793","bibliographicPageStart":"791","bibliographicVolumeNumber":"51","bibliographic_titles":[{"bibliographic_title":"Internal Medicine"}]}]},"item_4_description_21":{"attribute_name":"抄録","attribute_value_mlt":[{"subitem_description":"Hereditary motor sensory neuropathy type VI (HMSN VI) is hereditary neuropathy accompanied by optic neuropathy. The feasibility of Coenzyme Q10 (CoQ10) as a treatment for subacute visual impairment of HMSN VI was examined. A 37-year-old patient with HMSN VI with a novel mitofusin 2 mutation was treated with high dose of CoQ10 (200 mg/day) for eight months. Visual impairment was partially resolved after CoQ10 therapy. High dose CoQ10 therapy may improve the prognosis of subacute visual impairment in HMSN VI. To confirm the effectiveness of CoQ10 on HMSN VI, further studies are needed.","subitem_description_type":"Abstract"}]},"item_4_publisher_17":{"attribute_name":"出版者","attribute_value_mlt":[{"subitem_publisher":"Japanese Society of Internal Medicine = 日本内科学会"}]},"item_4_relation_12":{"attribute_name":"DOI","attribute_value_mlt":[{"subitem_relation_type":"isIdenticalTo","subitem_relation_type_id":{"subitem_relation_type_id_text":"10.2169/internalmedicine.51.6676","subitem_relation_type_select":"DOI"}}]},"item_4_relation_28":{"attribute_name":"関連URI","attribute_value_mlt":[{"subitem_relation_type_id":{"subitem_relation_type_id_text":"https://japanlinkcenter.org/JST.JSTAGE/internalmedicine/51.6676","subitem_relation_type_select":"URI"}},{"subitem_relation_type_id":{"subitem_relation_type_id_text":"http://www.naika.or.jp/","subitem_relation_type_select":"URI"}}]},"item_4_rights_23":{"attribute_name":"権利","attribute_value_mlt":[{"subitem_rights":"Copyright © 2012 by The Japanese Society of Internal Medicine"}]},"item_4_source_id_11":{"attribute_name":"NCID","attribute_value_mlt":[{"subitem_source_identifier":"AA10827774","subitem_source_identifier_type":"NCID"}]},"item_4_source_id_9":{"attribute_name":"ISSN","attribute_value_mlt":[{"subitem_source_identifier":"0918-2918","subitem_source_identifier_type":"ISSN"}]},"item_4_version_type_25":{"attribute_name":"著者版フラグ","attribute_value_mlt":[{"subitem_version_resource":"http://purl.org/coar/version/c_970fb48d4fbd8a85","subitem_version_type":"VoR"}]},"item_creator":{"attribute_name":"著者","attribute_type":"creator","attribute_value_mlt":[{"creatorNames":[{"creatorName":"Takahashi, Ryoichi"}],"nameIdentifiers":[{}]},{"creatorNames":[{"creatorName":"Ikeda, Tokuhei"}],"nameIdentifiers":[{}]},{"creatorNames":[{"creatorName":"Hamaguchi, Ayumi"}],"nameIdentifiers":[{}]},{"creatorNames":[{"creatorName":"Iwasa, Kazuo"}],"nameIdentifiers":[{},{},{}]},{"creatorNames":[{"creatorName":"Yamada, Masahito"}],"nameIdentifiers":[{},{},{},{}]}]},"item_files":{"attribute_name":"ファイル情報","attribute_type":"file","attribute_value_mlt":[{"accessrole":"open_date","date":[{"dateType":"Available","dateValue":"2017-10-03"}],"displaytype":"detail","filename":"HO-PR-TAKAHASHI-R-791.pdf","filesize":[{"value":"680.5 kB"}],"format":"application/pdf","licensetype":"license_note","mimetype":"application/pdf","url":{"label":"HO-PR-TAKAHASHI-R-791.pdf","url":"https://kanazawa-u.repo.nii.ac.jp/record/13652/files/HO-PR-TAKAHASHI-R-791.pdf"},"version_id":"f542774b-6d5f-41ec-bcbb-a13c92177865"}]},"item_language":{"attribute_name":"言語","attribute_value_mlt":[{"subitem_language":"eng"}]},"item_resource_type":{"attribute_name":"資源タイプ","attribute_value_mlt":[{"resourcetype":"journal article","resourceuri":"http://purl.org/coar/resource_type/c_6501"}]},"item_title":"Coenzyme Q10 Therapy in Hereditary Motor Sensory Neuropathy Type VI with Novel Mitofusin 2 Mutation","item_titles":{"attribute_name":"タイトル","attribute_value_mlt":[{"subitem_title":"Coenzyme Q10 Therapy in Hereditary Motor Sensory Neuropathy Type VI with Novel Mitofusin 2 Mutation"}]},"item_type_id":"4","owner":"3","path":["1134"],"pubdate":{"attribute_name":"公開日","attribute_value":"2017-10-03"},"publish_date":"2017-10-03","publish_status":"0","recid":"13652","relation_version_is_last":true,"title":["Coenzyme Q10 Therapy in Hereditary Motor Sensory Neuropathy Type VI with Novel Mitofusin 2 Mutation"],"weko_creator_id":"3","weko_shared_id":-1},"updated":"2023-07-28T01:00:53.459562+00:00"}