{"created":"2023-07-27T06:29:19.891374+00:00","id":14098,"links":{},"metadata":{"_buckets":{"deposit":"3da57ba9-5976-4dc2-8823-d4f1bf8e94a5"},"_deposit":{"created_by":3,"id":"14098","owners":[3],"pid":{"revision_id":0,"type":"depid","value":"14098"},"status":"published"},"_oai":{"id":"oai:kanazawa-u.repo.nii.ac.jp:00014098","sets":["1132:1133:1134"]},"author_link":["182","24047","24048","92"],"item_4_biblio_info_8":{"attribute_name":"書誌情報","attribute_value_mlt":[{"bibliographicIssueDates":{"bibliographicIssueDate":"2010-08-01","bibliographicIssueDateType":"Issued"},"bibliographicIssueNumber":"8","bibliographicPageEnd":"755","bibliographicPageStart":"749","bibliographicVolumeNumber":"31","bibliographic_titles":[{"bibliographic_title":"胆と膵 = The Biliary tract & pancreas"}]}]},"item_4_description_21":{"attribute_name":"抄録","attribute_value_mlt":[{"subitem_description":"原発性硬化性胆管炎(PSC)は硬化性胆管炎の原型である. 硬化性胆管炎の病態を示す患者では, 常にPSCとその類縁疾患と鑑別診断が必要である. PSCと鑑別を要する話題の疾患としてIgG4関連硬化性胆管炎がある. 本疾患は, 高率に自己免疫性膵炎に合併し, 病変部にIgG4陽性の形質細胞の浸潤と閉塞性静脈炎を認める. またPSCでは, 臨床的, 血清学的に自己免疫現象が出現し, インターフェイス肝炎や小葉炎を認めることがあり(自己免疫性肝炎(AIH)-PSCオーバーラップ症候群), 類縁疾患との鑑別診断が必要である. 特に, 小児PSCではAIH様の病態がしばしばみられ, AIHとPSCの鑑別が問題となる. 近年, 肝移植後のPSC再発が注目され, 予後不良の症例が多い. これらの症例, 特に若年例ではPSCの再発に加え, AIH類似の肝炎性の変化の合併が注目されている. PSCの病理学的な鑑別診断に関する最近の話題を中心に解説した.","subitem_description_type":"Abstract"}]},"item_4_publisher_17":{"attribute_name":"出版者","attribute_value_mlt":[{"subitem_publisher":"医学図書出版"}]},"item_4_relation_28":{"attribute_name":"関連URI","attribute_value_mlt":[{"subitem_relation_type_id":{"subitem_relation_type_id_text":"http://www.igakutosho.co.jp/","subitem_relation_type_select":"URI"}},{"subitem_relation_type_id":{"subitem_relation_type_id_text":"http://www.igakutosho.co.jp/magazine/t_s/2014/zt35s.html","subitem_relation_type_select":"URI"}}]},"item_4_rights_23":{"attribute_name":"権利","attribute_value_mlt":[{"subitem_rights":"Copyright © 医学図書出版 | 許可を得て登録"}]},"item_4_source_id_11":{"attribute_name":"NCID","attribute_value_mlt":[{"subitem_source_identifier":"AN00333226","subitem_source_identifier_type":"NCID"}]},"item_4_source_id_9":{"attribute_name":"ISSN","attribute_value_mlt":[{"subitem_source_identifier":"0388-9408","subitem_source_identifier_type":"ISSN"}]},"item_4_text_2":{"attribute_name":"その他のタイトル","attribute_value_mlt":[{"subitem_text_value":"[特集]原発性硬化性胆管炎の最近の話題"},{"subitem_text_value":"Topics of Primary Sclerosing Cholangitis: Differential Diagnosis with Respect to Pathologic Features"}]},"item_4_version_type_25":{"attribute_name":"著者版フラグ","attribute_value_mlt":[{"subitem_version_resource":"http://purl.org/coar/version/c_970fb48d4fbd8a85","subitem_version_type":"VoR"}]},"item_creator":{"attribute_name":"著者","attribute_type":"creator","attribute_value_mlt":[{"creatorNames":[{"creatorName":"中沼, 安二"}],"nameIdentifiers":[{},{},{}]},{"creatorNames":[{"creatorName":"原田, 憲一"}],"nameIdentifiers":[{},{},{},{}]},{"creatorNames":[{"creatorName":"宮川, 文"}],"nameIdentifiers":[{}]},{"creatorNames":[{"creatorName":"羽賀, 博典"}],"nameIdentifiers":[{}]}]},"item_files":{"attribute_name":"ファイル情報","attribute_type":"file","attribute_value_mlt":[{"accessrole":"open_date","date":[{"dateType":"Available","dateValue":"2017-10-03"}],"displaytype":"detail","filename":"ME-PR-NAKANUMA-Y-749.pdf","filesize":[{"value":"6.4 MB"}],"format":"application/pdf","licensetype":"license_note","mimetype":"application/pdf","url":{"label":"ME-PR-NAKANUMA-Y-749.pdf","url":"https://kanazawa-u.repo.nii.ac.jp/record/14098/files/ME-PR-NAKANUMA-Y-749.pdf"},"version_id":"44d5d2b2-86d4-4bf0-b4e3-036a0d323d25"}]},"item_language":{"attribute_name":"言語","attribute_value_mlt":[{"subitem_language":"jpn"}]},"item_resource_type":{"attribute_name":"資源タイプ","attribute_value_mlt":[{"resourcetype":"journal article","resourceuri":"http://purl.org/coar/resource_type/c_6501"}]},"item_title":"病理像による原発性硬化性胆管炎の鑑別診断","item_titles":{"attribute_name":"タイトル","attribute_value_mlt":[{"subitem_title":"病理像による原発性硬化性胆管炎の鑑別診断"}]},"item_type_id":"4","owner":"3","path":["1134"],"pubdate":{"attribute_name":"公開日","attribute_value":"2017-10-03"},"publish_date":"2017-10-03","publish_status":"0","recid":"14098","relation_version_is_last":true,"title":["病理像による原発性硬化性胆管炎の鑑別診断"],"weko_creator_id":"3","weko_shared_id":-1},"updated":"2023-07-28T00:53:01.416060+00:00"}