@article{oai:kanazawa-u.repo.nii.ac.jp:00026978, author = {Kim, Fae and Yamada, Kazunori and Inoue, Dai and Nakajima, Kenichi and Mizushima, Ichiro and Kakuchi, Yasushi and Fujii, Hiroshi and Narumi, Kenta and Matsumura, Masami and Umehara, Hisanori and Yamagishi, Masakazu and Kawano, Mitsuhiro}, issue = {11}, journal = {Internal Medicine}, month = {Jan}, note = {Immunoglobulin G4 (IgG4)-related tubulointerstitial nephritis (TIN) is often accompanied by autoimmune pancreatitis (AIP) or chronic sclerosing dacryoadenitis and sialoadenitis. However, IgG4-related TIN without AIP or lacrimal and/or salivary gland lesions has not been well recognized. Here, we report a case of IgG4-related TIN associated with hepatic inflammatory pseudotumor without AIP or lacrimal and/or salivary gland lesions. A 58-year-old Japanese man with epigastralgia underwent contrast-enhanced computed tomography (CT), which revealed multiple low-density lesions in both kidneys and a low density hepatic mass. Laboratory tests showed an extremely high level of serum IgG4. Percutaneous renal and hepatic biopsies showed diffuse infiltration of lymphocytes and IgG4-positive plasma cells with fibrosis in both tissues. Two months after administration of oral prednisolone, both lesions decreased in size on follow-up CT, and the serum cre-atinine level also improved. No recurrence has been detected for two years with a maintenance dose of pred-nisolone. © 2011 The Japanese Society of Internal Medicine., 金沢大学附属病院リウマチ・膠原病内科}, pages = {1239--1244}, title = {IgG4-related tubulointerstitial nephritis and hepatic inflammatory pseudotumor without hypocomplementemia}, volume = {50}, year = {2011} }