@article{oai:kanazawa-u.repo.nii.ac.jp:00055613, author = {中沼, 伸一 and 高村, 博之 and 林, 泰寛 and 田島, 秀浩 and 中川原, 寿俊 and 宮下, 知治 and 北川, 裕久 and 太田, 哲生 and Nakanuma, Shinichi and Takamura, Hiroyuki and Shoji, Masatoshi and Hayashi, Hironori and Tajima, Hidehiro and Nakagawara, Hisatoshi and Miyashita, Tomoharu and Kitagawa, Hirohisa and Tani, Takashi and Ohta, Tetsuo}, issue = {5}, journal = {Experimental and Clinical Transplantation}, month = {Sep}, note = {Liver transplant is a treatment for familial amyloid polyneuropathy. Few cases of ABO-incompatible living-donor liver transplant for familial amyloid polyneuropathy exist. The outcome of an ABO-incompatible living-donor liver transplant has improved recently, using local infusion therapy and rituximab prophylaxis. Here, we describe a successful ABO-incompatible living-donor liver transplant in a patient with familial amyloid polyneuropathy in whom disease progression ceased at 2 years’ follow-up. Additionally, no evidence of acute or chronic rejection, or adverse events of the immuno-suppressive therapy, was seen. As a postoperative complication, fatty changes in the grafted liver because of malnutrition or adverse events of corticosteroids were confirmed by a liver biopsy taken early after transplant. The main cause of malnutrition was considered to be gastrointestinal dysfunction caused by familial amyloid poly-neuropathy. Therefore, before deterioration of digestive function, liver transplants should be considered for familial amyloid polyneuropathy. This case suggests that an ABO-incompatible living-donor liver transplant may provide greater opportunities for familial amyloid polyneuropathy patients., 金沢大学附属病院肝胆膵・移植外科}, pages = {479--481}, title = {Case Report of an ABO-Incompatible Living-Donor Liver Transplant for a Familial Amyloid Polyneuropathy Patient}, volume = {13}, year = {2014} }